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Bruce W. Konigsmark, MD; Mark B. Hollander, MD; Charles I. Berlin, PhD

JAMA. 1968;204(11):953-957.

Abstract
Three of four sibs were affected by a nonprogressive neural hearing loss and atypical atopic dermatitis. History, physical and neurological examinations revealed no causes other than familial for the hearing loss. Audiometric examinations suggested the hearing loss was cochlear in origin. A review of the literature describing types of familial hearing loss associated with skin disease showed no similar report. It is suggested that these three children have a type of recessive familial hearing loss differing from others in its association with atypical atopic dermatitis.

Author Affiliations
From the divisions of laryngology and otology and dermatology and the Department of Pathology, the Johns Hopkins University School of Medicine, Baltimore. Dr. Berlin is now with the Louisiana State University School of Medicine, New Orleans.

Footnotes
Read in part before the Second International Congress of Neurogenetics and Neuro-ophthalmology of the World Federation of Neurology, Montreal, Sept 19, 1967.

Reprint requests to the Johns Hopkins Hospital, Baltimore 21205 (Dr. Konigsmark).

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