Alpha-1-antitrypsin deficiency, emphysema, cirrhosis, and intestinal mucosal atrophy

A. J. Greenwald, D. S. Johnson, R. M. Oskvig, C. A. Aschenbrener and D. C. Randa

An elderly man with long-standing pulmonary emphysema was seen with recent onset of steatorrhea and ascites. He had very low levels of serum alpha1-antitrypsin, hepatic cirrhosis, and intestinal mucosal atrophy. We believe this this combination of findings did not occur by chance.

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