Lymphangiomatosis with splenic involvement
S. Avigad, R. Jaffe, M. Frand, Y. Izhak and Y. Rotem
Severe splenomegaly and anemia developed in a 5-year-old girl with diffuse
lymphangiomatosis of the upper part of the body. Radioisotope scanning and
celiac angiography demonstrated lymphangiomatosis of the spleen, a rare but
diagnosable condition. Intractable infection in areas of ulcerated skin led
to her death from overwhelming sepsis.
