Asplenia syndrome. A study of congenital anomalies in 16 cases
J. A. Majeski and J. K. Upshur
Sixteen new cases of the asplenia syndrome with autopsy findings had a
female preponderance of 2:1. Racial incidence of splenic agenesis was nine
whites and seven blacks. The average life span of the infants born alive
was approximately 38 days. All infants with the asplenia syndrome had
recorded weights and lengths below normal standard values. Surgical
palliation of the cardiovascular anomalies in the asplenia syndrome was
attempted in two cases. The incidence of the asplenia syndrome from the
large autopsy series at the Medical University of South Carolina is one
case per 2,000 autopsies.
